I've never encountered this situation... but I'm really curious. What are normal vitals for a little person? Can you use an AED... if so... what pads? Are there any special considerations as far as immobilization?
neither have i, but i can take a crack at your questions:
1: havent the foggiest idea, but would be interested in the answer
2a: without a doubt
2b: the aha, to the best of my knowledge(i have been an instructor fo r4 years), has never specifically covered this issue in any of its classroom literature since i started teaching. i personally would handle it much like i would determining whether to use pedi pads or adult pads on a 7 year old. if its a particularly monstorous 7 year old, one might be inclined to use the adult pads, since they are really the size of an 8 year old(or bigger etc). thus, the reverse is true. what if and 8 year old is tiny, very underdeveloped. he gets pedi pads.your dwarf will probably buy some adult pads, assuming they dont overlap etc.
3: consider putting two patients on one backboardif its an mci....
I actually have encountered this many years ago when I had a Dwarf that was in cardiac arrest. The Intermediates questioned if they could use an EOA due to the size? Dwarfism is a genetic disorder where the parts of the body are normal such as head and hands, feet. Where as midget is proportionally small.
Like all patients treat according to age development and size.
Anyone have any idea of differences in vitals? I would think that their vitals would resemble those of a child of similar size... but I imagine there may some differences due to age.
Thanks for all the great responses by the way! This has been the "hm?" question on my mind for a couple of weeks.
I would be interested to see those stats as well. It's my understanding and I may be wrong, that dwarfism is a condition affecting the long bones only. That is why head, hands, rib cage and torso etc remain full sized. To me, that would mean that the internal organs, and vital signs should be the same as an average size adult. But, I'm theorizing only and have nothing official to base it on.
Well I emailed the medical resource center of Little People of America to see if they have any information on the subject. I'll let you know if they respond.
BossyCow... I believe you're correct about the extremities alone being affected in most cases of dwarfism, but I think there are other forms of the disease that affect the entire body. It does make sense that those with "traditional" dwarfism would have adult vitals though, perhaps with a slightly lower blood pressure because their heart wouldn't have to pump blood as far as it would in an adult with longer arms and legs? I'm not really sure.
Dwarfism can be caused by several factors. Hormonal, pituitary disorders, or a disorder called Hanhart syndrome type IV. This a rare disorder where a genetic error of amino acid metabolism results in thickened skin on palms and soles, skin lumps, mental retardation and finger, toe, eye, hair and teeth abnormalities.
But isn't that the underlying issue here? The age/size ratio is disproportionate.
On top of that, I'd be curious to find out if liver and renal function are affected by this disorder.
I am a person with dwarfism this specific type SEMDJL type two
You would be cautious with medication according to weight
You would be cautious with anesthesia due to C1 C2 instability
Organs are normal, mental abilities is normal
Mostly a bones and joint cartilage disorder.
Had one child with laryngotracheomalacia
Had a trach and passed away at eight months.
Vitals I believe are normal for height and weight. Eight mine happens to be 100/60.
Anybody working in medical community should be educated for all types of people!
I hope this answers some of your questions
Spondyloepimetaphyseal
dysplasia with joint laxity, 2
bone disease characterized by short stature, distinctive midface retrusion, progressive knee malalignment (genu valgum and/or varum), generalized ligamentous laxity, and mild spinal deformity. Intellectual development is not impaired. Radiographic characteristics include significantly retarded epiphyseal ossification that evolves into epiphyseal dysplasia and precocious osteoarthritis, metaphyseal irregularities and vertical striations, constricted femoral neck, slender metacarpals and metatarsals, and mild thoracolumbar kyphosis or scoliosis with normal or mild platyspondyly. The most distinctive features for differential diagnosis of SEMDJL2 are the slender metacarpals and phalanges and the progressive degeneration of carpal bones; however, these 2 features are evident only in older children and young adults. The soft consistency of cartilage in the airways leads to laryngotracheomalacia with proneness to respiratory obstruction and inspiratory stridor in infancy and childhood.
SEMDJL2
Lepto-SEMDJL
Spondyloepimetaphyseal dysplasia with joint laxity Hall type
Spondyloepimetaphyseal dysplasia: with joint laxity leptodactylic type Spondyloepimetaphyseal dysplasia with multiple dislocations Hall type
